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NDUFB4 [mitochondrial inner membrane]
Stable Identifier
R-HSA-59934
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase B15 subunit , Complex I-B15, CI-B15
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
The citric acid (TCA) cycle and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB4 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB4 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB4 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB4 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB4 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB4 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB4 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB4 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB4 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB4 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB4 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB4 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB4 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O95168 NDUFB4
Gene Names
NDUFB4
Chain
initiator methionine:, chain:2-129
Reference Genes
BioGPS Gene:4710 NDUFB4
COSMIC (genes):NDUFB4 NDUFB4
CTD Gene:4710 NDUFB4
dbSNP Gene:4710 NDUFB4
ENSEMBL:ENSG00000065518 NDUFB4
ENSEMBL_homo_sapiens_GENE:ENSG00000065518.8 NDUFB4
HGNC:7699 NDUFB4
KEGG Gene (Homo sapiens):4710 NDUFB4
Monarch:4710 NDUFB4
NCBI Gene:4710 NDUFB4
OMIM:603840 NDUFB4
UCSC:O95168 NDUFB4
Reference Transcript
RefSeq:NM_004547.5 NDUFB4
RefSeq:NM_001168331.1 NDUFB4
Other Identifiers
11718278_s_at
11745384_s_at
11760040_x_at
16944502
218226_PM_s_at
218226_s_at
228940_PM_at
228940_at
2638440
2638441
2638449
2638450
2638451
2638452
2638453
4047218
4047219
4047220
4047221
4047222
4047227
4047228
4710
65777_at
65778_at
8081945
8093314
A_23_P69468
GE61710
GE79271
GE87765
GO:0003824
GO:0005215
GO:0005634
GO:0005654
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0006979
GO:0007005
GO:0008137
GO:0009060
GO:0016020
GO:0016491
GO:0032981
GO:0042776
GO:0043226
GO:0055086
GO:0065003
GO:0070469
GO:1901135
HMNXSV003051864
Hs.227750.1.S1_3p_a_at
Hs.227750.1.S1_3p_x_at
ILMN_1668027
ILMN_1721719
ILMN_2081863
PH_hs_0012660
PH_hs_0026966
TC03000617.hg
g6041668_3p_a_at
Participates
as a component of
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
Inferred To
ndufb4 [mitochondrial inner membrane]
(Xenopus tropicalis)
LOC103691107 [mitochondrial inner membrane]
(Rattus norvegicus)
nuo-6 [mitochondrial inner membrane]
(Caenorhabditis elegans)
NDUFB4 [mitochondrial inner membrane]
(Bos taurus)
NDUFB4 [mitochondrial inner membrane]
(Canis familiaris)
NDUFB4 [mitochondrial inner membrane]
(Gallus gallus)
NDUFB4 [mitochondrial inner membrane]
(Sus scrofa)
Ndufb4 [mitochondrial inner membrane]
(Mus musculus)
ND-B15 [mitochondrial inner membrane]
(Drosophila melanogaster)
fj49f11 [mitochondrial inner membrane]
(Danio rerio)
Cross References
RefSeq
NP_004538.2
,
NP_001161803.1
OpenTargets
ENSG00000065518
HPA
ENSG00000065518-NDUFB4
GeneCards
O95168
Ensembl
ENST00000485064
,
ENSG00000065518
,
ENSP00000184266
,
ENSP00000419578
,
ENST00000184266
PRO
O95168
Pharos - Targets
O95168
HMDB Protein
HMDBP00149
PDB
5XTI
,
5XTC
,
5XTH
,
5XTD
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.527
5
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