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NDUFA3 [mitochondrial inner membrane]
Stable Identifier
R-HSA-60180
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase B9 subunit , Complex I-B9, CI-B9
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O95167 NDUFA3
Gene Names
NDUFA3
Chain
initiator methionine:, chain:2-84
Reference Genes
BioGPS Gene:4696 NDUFA3
COSMIC (genes):NDUFA3 NDUFA3
CTD Gene:4696 NDUFA3
dbSNP Gene:4696 NDUFA3
ENSEMBL:ENSG00000170906 NDUFA3
HGNC:7686 NDUFA3
KEGG:hsa:4696 NDUFA3
Monarch:4696 NDUFA3
NCBI Gene:4696 NDUFA3
OMIM:603832 NDUFA3
UCSC:O95167 NDUFA3
Reference Transcript
RefSeq:XM_017026833.1 NDUFA3
RefSeq:NM_004542.3 NDUFA3
Other Identifiers
11723467_a_at
11753843_a_at
11753844_x_at
11761806_a_at
16865175
218563_PM_at
218563_at
3841199
3841200
3841201
3841208
3841209
3841210
3841211
3841212
3841213
3841214
3841215
3841216
3841217
3841218
3841219
3841220
3841221
3841222
4696
63791_at
72138_at
8031097
A_23_P208540
GE79970
GO:0003824
GO:0005215
GO:0005515
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0008137
GO:0009060
GO:0016020
GO:0016491
GO:0032981
GO:0042776
GO:0043226
GO:0045271
GO:0055085
GO:0055086
GO:0065003
GO:1901135
GO:1902600
HMNXSV003033108
ILMN_1784641
PH_hs_0029413
g4758771_3p_at
Participates
as a component of
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
Inferred To
NDUFA3 [mitochondrial inner membrane]
(Bos taurus)
NDUFA3 [mitochondrial inner membrane]
(Canis familiaris)
NDUFA3 [mitochondrial inner membrane]
(Sus scrofa)
Ndufa3 [mitochondrial inner membrane]
(Mus musculus)
Ghost homologue of NDUFA3 [mitochondrial inner membrane]
(Caenorhabditis elegans)
Ghost homologue of NDUFA3 [mitochondrial inner membrane]
(Danio rerio)
Ghost homologue of NDUFA3 [mitochondrial inner membrane]
(Drosophila melanogaster)
Ghost homologue of NDUFA3 [mitochondrial inner membrane]
(Gallus gallus)
Ghost homologue of NDUFA3 [mitochondrial inner membrane]
(Xenopus tropicalis)
Ndufa3-ps3 [mitochondrial inner membrane]
(Rattus norvegicus)
Cross References
OpenTargets
ENSG00000170906
ENSEMBL
ENSP00000477919
,
ENST00000621307
,
ENST00000620289
,
ENST00000619253
,
ENST00000617282
,
ENST00000485876
,
ENSP00000398290
,
ENSP00000480437
,
ENSP00000484436
,
ENSP00000481545
,
ENSP00000483934
,
ENSP00000482015
,
ENST00000610406
,
ENST00000612327
,
ENSP00000477783
,
ENST00000419113
,
ENST00000619966
,
ENST00000618338
,
ENSP00000483002
,
ENSP00000483683
,
ENST00000622523
,
ENST00000613276
,
ENSP00000478119
,
ENSP00000418438
HPA
ENSG00000170906-NDUFA3
PRO
O95167
Pharos - Targets
O95167
HMDB Protein
HMDBP00129
PDB
5XTH
,
5XTI
,
5XTC
,
5XTD
Interactors (8)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q8N4V1 MMGT1
1
MMGT1 [Golgi membrane]
(R-HSA-5216137)
0.666
4
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.643
5
UniProt:Q15125 EBP
1
EBP [endoplasmic reticulum membrane]
(R-HSA-195697)
0.556
3
UniProt:Q9P0J0 NDUFA13
8
NDUFA13 [mitochondrial inner membrane]
(R-HSA-59936)
NDUFA13(41-49) [mitochondrial inner membrane]
(R-HSA-9839958)
NDUFA13(100-108) [mitochondrial inner membrane]
(R-HSA-9839959)
NDUFA13(109-144) [mitochondrial inner membrane]
(R-HSA-9839968)
NDUFA13(2-19) [mitochondrial inner membrane]
(R-HSA-9839966)
NDUFA13(69-99) [mitochondrial inner membrane]
(R-HSA-9839964)
NDUFA13(20-40) [mitochondrial inner membrane]
(R-HSA-9839963)
NDUFA13(50-68) [mitochondrial inner membrane]
(R-HSA-9839961)
0.527
3
UniProt:Q9BQ95 ECSIT
2
ECSIT [cytosol]
(R-HSA-168064)
ECSIT [mitochondrial inner membrane]
(R-HSA-5689047)
0.527
2
UniProt:O75380 NDUFS6
1
NDUFS6 [mitochondrial inner membrane]
(R-HSA-163922)
0.527
4
UniProt:Q99999 GAL3ST1
1
GAL3ST1 [Golgi membrane]
(R-HSA-1631586)
0.527
3
UniProt:P01019 AGT
7
AGT(36-41) [extracellular region]
(R-HSA-2022355)
AGT(35-41) [extracellular region]
(R-HSA-2022354)
AGT(34-40) [extracellular region]
(R-HSA-2022351)
AGT(34-42) [extracellular region]
(R-HSA-2022348)
AGT [extracellular region]
(R-HSA-1998759)
AGT(34-43) [extracellular region]
(R-HSA-2022346)
AGT(34-41) [extracellular region]
(R-HSA-374187)
0.527
2
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