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NDUFA3 [mitochondrial inner membrane]
Stable Identifier
R-HSA-60180
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase B9 subunit , Complex I-B9, CI-B9
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
The citric acid (TCA) cycle and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA3 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O95167 NDUFA3
Gene Names
NDUFA3
Chain
initiator methionine:, chain:2-84
Reference Genes
BioGPS Gene:4696 NDUFA3
COSMIC (genes):NDUFA3 NDUFA3
CTD Gene:4696 NDUFA3
dbSNP Gene:4696 NDUFA3
ENSEMBL:ENSG00000170906 NDUFA3
ENSEMBL_homo_sapiens_GENE:ENSG00000170906.16 NDUFA3
ENSEMBL_homo_sapiens_GENE:ENSG00000273642.1 NDUFA3
ENSEMBL_homo_sapiens_GENE:ENSG00000274359.1 NDUFA3
ENSEMBL_homo_sapiens_GENE:ENSG00000275605.1 NDUFA3
ENSEMBL_homo_sapiens_GENE:ENSG00000275724.1 NDUFA3
ENSEMBL_homo_sapiens_GENE:ENSG00000276061.4 NDUFA3
ENSEMBL_homo_sapiens_GENE:ENSG00000276220.1 NDUFA3
ENSEMBL_homo_sapiens_GENE:ENSG00000276766.1 NDUFA3
ENSEMBL_homo_sapiens_GENE:ENSG00000277722.1 NDUFA3
ENSEMBL_homo_sapiens_GENE:ENSG00000278365.1 NDUFA3
HGNC:7686 NDUFA3
KEGG Gene (Homo sapiens):4696 NDUFA3
Monarch:4696 NDUFA3
NCBI Gene:4696 NDUFA3
OMIM:603832 NDUFA3
Reference Transcript
RefSeq:NM_004542.3 NDUFA3
RefSeq:XM_017026833.1 NDUFA3
Other Identifiers
11723467_a_at
11753843_a_at
11753844_x_at
11761806_a_at
16865175
218563_PM_at
218563_at
3841199
3841201
3841209
3841210
3841215
3841216
3841217
3841218
3841219
3841220
4696
63791_at
72138_at
8031097
A_23_P208540
GE79970
GO:0003824
GO:0005215
GO:0005515
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0007005
GO:0008137
GO:0009060
GO:0016020
GO:0016491
GO:0032981
GO:0042776
GO:0043226
GO:0055086
GO:0065003
GO:0070469
GO:1901135
HMNXSV003033108
ILMN_1784641
PH_hs_0029413
g4758771_3p_at
Participates
as a component of
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
Inferred To
NDUFA3 [mitochondrial inner membrane]
(Bos taurus)
NDUFA3 [mitochondrial inner membrane]
(Canis familiaris)
NDUFA3 [mitochondrial inner membrane]
(Sus scrofa)
Ndufa3 [mitochondrial inner membrane]
(Mus musculus)
Ghost homologue of NDUFA3 [mitochondrial inner membrane]
(Caenorhabditis elegans)
Ghost homologue of NDUFA3 [mitochondrial inner membrane]
(Danio rerio)
Ghost homologue of NDUFA3 [mitochondrial inner membrane]
(Drosophila melanogaster)
Ghost homologue of NDUFA3 [mitochondrial inner membrane]
(Gallus gallus)
Ghost homologue of NDUFA3 [mitochondrial inner membrane]
(Xenopus tropicalis)
Ndufa3-ps3 [mitochondrial inner membrane]
(Rattus norvegicus)
Cross References
RefSeq
XP_016882322.1
,
NP_004533.1
OpenTargets
ENSG00000170906
GeneCards
O95167
HPA
ENSG00000170906-NDUFA3
Ensembl
ENSG00000275605
,
ENSG00000275724
,
ENST00000419113
,
ENSG00000276220
,
ENSG00000278365
,
ENST00000617282
,
ENSG00000276766
,
ENSP00000477919
,
ENSG00000273642
,
ENSG00000274359
,
ENSG00000170906
,
ENST00000613276
,
ENST00000621307
,
ENST00000619253
,
ENSP00000483934
,
ENST00000610406
,
ENST00000612327
,
ENST00000622523
,
ENSP00000418438
,
ENST00000620289
,
ENST00000485876
,
ENSP00000482015
,
ENSP00000484436
,
ENSP00000483002
,
ENSP00000483683
,
ENSP00000480437
,
ENSP00000481545
,
ENSP00000478119
,
ENSG00000276061
,
ENSG00000277722
,
ENST00000618338
,
ENSP00000477783
,
ENSP00000398290
,
ENST00000619966
PRO
O95167
Pharos - Targets
O95167
Orphanet
24737
HMDB Protein
HMDBP00129
PDB
5XTH
,
5XTD
,
5XTI
,
5XTC
Interactors (3)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q8N4V1 MMGT1
1
MMGT1 [Golgi membrane]
(R-HSA-5216137)
0.556
3
UniProt:Q15125 EBP
1
EBP [endoplasmic reticulum membrane]
(R-HSA-195697)
0.556
3
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.527
4
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