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PXLP-OAT(26-439) [mitochondrial matrix]
Stable Identifier
R-HSA-70638
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
ornithine aminotransferase, mitochondrial, OAT, ornithine-oxo-acid aminotransferase
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Glutamate and glutamine metabolism (Homo sapiens)
glutamate + L-glutamate gamma-semialdehyde <=> ornithine + alpha-ketoglutarate [OAT] (Homo sapiens)
OAT hexamer [mitochondrial matrix] (Homo sapiens)
PXLP-OAT(26-439) [mitochondrial matrix] (Homo sapiens)
ornithine + alpha-ketoglutarate <=> glutamate + L-glutamate gamma-semialdehyde [OAT] (Homo sapiens)
OAT hexamer [mitochondrial matrix] (Homo sapiens)
PXLP-OAT(26-439) [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:P04181 OAT
Gene Names
OAT
Chain
transit peptide:1-35, transit peptide:1-25, chain:26-439, chain:36-439
Reference Genes
BioGPS Gene:4942 OAT
COSMIC (genes):OAT OAT
CTD Gene:4942 OAT
dbSNP Gene:4942 OAT
ENSEMBL:ENSG00000065154 OAT
HGNC:8091 OAT
KEGG:hsa:4942 OAT
Monarch:4942 OAT
NCBI Gene:4942 OAT
OMIM:613349 OAT
UCSC:P04181 OAT
Reference Transcript
RefSeq:NM_001322970.1 OAT
RefSeq:NM_001171814.1 OAT
RefSeq:NM_000274.3 OAT
RefSeq:NM_001322969.1 OAT
RefSeq:NM_001322967.1 OAT
RefSeq:NM_001322971.1 OAT
RefSeq:NM_001322965.1 OAT
RefSeq:NM_001322968.1 OAT
RefSeq:NM_001322966.1 OAT
Other Identifiers
11757997_s_at
16719233
201599_PM_at
201599_at
3311159
3311160
3311161
3311162
3311163
3311164
3311165
3311166
3311167
3311168
3311169
3311170
3311171
3311172
3311173
3311174
3311175
3311176
3311178
3311179
3311180
3311181
3311183
36636_at
3976599
3976600
4007325
4007408
4007414
4942
7936871
A_23_P98092
GE57811
GO:0003824
GO:0004587
GO:0005515
GO:0005654
GO:0005737
GO:0005739
GO:0005759
GO:0006520
GO:0007601
GO:0008483
GO:0010121
GO:0016740
GO:0019544
GO:0030170
GO:0042802
GO:0043226
GO:0050877
GO:0055129
HMNXSV003019730
ILMN_1654441
ILMN_2068747
M29927_at
PH_hs_0004331
TC10001726.hg
g4557808_3p_at
Participates
as a component of
OAT hexamer [mitochondrial matrix] (Homo sapiens)
Inferred To
oat [mitochondrial matrix]
(Xenopus tropicalis)
car2 [mitochondrial matrix]
(Schizosaccharomyces pombe)
Oat [mitochondrial matrix]
(Drosophila melanogaster)
Oat [mitochondrial matrix]
(Mus musculus)
Oat [mitochondrial matrix]
(Rattus norvegicus)
oatr-1 [mitochondrial matrix]
(Caenorhabditis elegans)
OAT [mitochondrial matrix]
(Bos taurus)
OAT [mitochondrial matrix]
(Canis familiaris)
OAT [mitochondrial matrix]
(Gallus gallus)
OAT [mitochondrial matrix]
(Plasmodium falciparum)
OAT [mitochondrial matrix]
(Sus scrofa)
CAR2 [mitochondrial matrix]
(Saccharomyces cerevisiae)
oatA [mitochondrial matrix]
(Dictyostelium discoideum)
Modified Residues
Name
N6-pyridoxal phosphate-L-lysine at 292
Coordinate
292
PsiMod Name
N6-pyridoxal phosphate-L-lysine [MOD:00128]
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to N6-pyridoxal phosphate-L-lysine.
Cross References
OpenTargets
ENSG00000065154
ENSEMBL
ENST00000368845
,
ENSP00000439042
,
ENSP00000357838
,
ENST00000539214
IntEnz
2.6.1.13
HPA
ENSG00000065154-OAT
PRO
P04181
Pharos - Targets
P04181
Orphanet
OAT
GlyGen
P04181
HMDB Protein
HMDBP00400
PDB
7TA0
,
2OAT
,
7TA1
,
2CAN
,
8V9M
,
7LOM
,
5VWO
,
7LON
,
7JX9
,
1GBN
,
7TED
,
7TEV
,
7LNM
,
7LK0
,
7LK1
,
7T9Z
,
7TFP
,
8EZ1
,
6V8C
,
6HX7
,
6V8D
,
6OIA
,
1OAT
,
2BYJ
,
2BYL
Interactors (2)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P05067 APP
20
APP(672-713) [extracellular region]
(R-HSA-879340)
APP(672-711) [cytosol]
(R-HSA-877188)
APP(672-711) [extracellular region]
(R-HSA-976740)
APP [endoplasmic reticulum lumen]
(R-HSA-8956696)
p-APP [endoplasmic reticulum lumen]
(R-HSA-8957012)
APP(18-770) [endosome lumen]
(R-HSA-5229077)
APP(672-711) [endosome lumen]
(R-HSA-6783333)
APP(672-713) [endosome lumen]
(R-HSA-5692993)
APP(672-770) [endosome lumen]
(R-HSA-9010082)
APP(712-770) [endosome lumen]
(R-HSA-6783331)
APP(714-770) [endosome lumen]
(R-HSA-6783325)
APP(18-671) [endosome lumen]
(R-HSA-5693003)
APP(18-770) [plasma membrane]
(R-HSA-9010038)
APP(18-770) [Golgi lumen]
(R-HSA-8871509)
APP(688-770) [plasma membrane]
(R-HSA-9010028)
APP(18-687) [extracellular region]
(R-HSA-9010033)
APP(18-770) [platelet alpha granule lumen]
(R-HSA-139835)
APP(18-770) [extracellular region]
(R-HSA-49335)
APP-C99 [cytosol]
(R-HSA-9617603)
APP(18-770) [trans-Golgi network membrane]
(R-HSA-5229136)
0.556
3
UniProt:P13569 CFTR
17
misfolded CFTR [endoplasmic reticulum membrane]
(R-HSA-8868730)
CFTR [endoplasmic reticulum membrane]
(R-HSA-8866837)
CFTR [plasma membrane]
(R-HSA-383188)
CFTR N1303K [plasma membrane]
(R-HSA-5678983)
CFTR F508del [plasma membrane]
(R-HSA-5678978)
CFTR W1282* [plasma membrane]
(R-HSA-5678976)
CFTR G551D [plasma membrane]
(R-HSA-5678977)
CFTR G542* [plasma membrane]
(R-HSA-5678986)
ub-CFTR F508del [endoplasmic reticulum membrane]
(R-HSA-8866842)
ub-CFTR F508del [cytosol]
(R-HSA-8866838)
CFTR F508del [endoplasmic reticulum membrane]
(R-HSA-8866834)
PolyUb-CFTR [endosome membrane]
(R-HSA-6782976)
CFTR [endosome membrane]
(R-HSA-6782965)
CFTR [Golgi-associated vesicle membrane]
(R-HSA-5627079)
CFTR [lysosomal membrane]
(R-HSA-5627279)
PolyUb-CFTR [plasma membrane]
(R-HSA-8867595)
PolyUb-CFTR [clathrin-coated endocytic vesicle membrane]
(R-HSA-8869104)
0.483
5
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