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IVD [mitochondrial matrix]
Stable Identifier
R-HSA-70729
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
isovaleryl-CoA dehydrogenase, apoenzyme, IVD_HUMAN, Isovaleryl-CoA dehydrogenase, mitochondrial precursor
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Branched-chain amino acid catabolism (Homo sapiens)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Homo sapiens)
IVD tetramer [mitochondrial matrix] (Homo sapiens)
IVD [mitochondrial matrix] (Homo sapiens)
Literature References
PubMed ID
Title
Journal
Year
9214289
Structure of human isovaleryl-CoA dehydrogenase at 2.6 A resolution: structural basis for substrate specificity,.
Wang, M
,
Paschke, R
,
Tiffany, KA
,
Roberts, DL
,
Kim, JJ
,
Mohsen, AW
,
Vockley, J
Biochemistry
1997
External Reference Information
External Reference
UniProt:P26440 IVD
Gene Names
IVD
Chain
transit peptide:1-32, chain:33-426
Reference Genes
BioGPS Gene:3712 IVD
COSMIC (genes):IVD IVD
CTD Gene:3712 IVD
dbSNP Gene:3712 IVD
ENSEMBL:ENSG00000128928 IVD
ENSEMBL_homo_sapiens_GENE:ENSG00000128928.10 IVD
HGNC:6186 IVD
KEGG Gene (Homo sapiens):3712 IVD
Monarch:3712 IVD
NCBI Gene:3712 IVD
OMIM:607036 IVD
UCSC:P26440 IVD
Reference Transcript
RefSeq:NM_002225.3 IVD
RefSeq:NM_001159508.1 IVD
Other Identifiers
11720642_a_at
11720643_a_at
16799538
203682_PM_s_at
203682_s_at
216958_PM_s_at
216958_s_at
225311_PM_at
225311_at
3589906
3589907
3589908
3589910
3589912
3589915
3589916
3589918
3589919
3589921
3589924
3589926
3589927
3589928
3589930
3589931
3589932
3589933
3589934
3589935
3589936
3589937
3589938
3712
37342_s_at
63548_at
78746_at
7982723
A_23_P129313
A_23_P129322
A_33_P3269718
GE58276
GO:0003824
GO:0003995
GO:0004085
GO:0005515
GO:0005634
GO:0005654
GO:0005739
GO:0005759
GO:0006520
GO:0006552
GO:0006629
GO:0006631
GO:0008470
GO:0009083
GO:0016491
GO:0016627
GO:0016937
GO:0033539
GO:0042802
GO:0043226
GO:0050660
GO:1901565
HMNXSV003025668
HMNXSV003033658
HMNXSV003042078
Hs.279789.5.A1_3p_at
Hs.279789.5.A1_3p_x_at
Hs.77510.2.S1_3p_a_at
ILMN_1724207
M34192_at
PH_hs_0024828
TC15000284.hg
g6031167_3p_a_at
Participates
as a component of
IVD tetramer [mitochondrial matrix] (Homo sapiens)
Inferred To
IVD [mitochondrial matrix]
(Bos taurus)
IVD [mitochondrial matrix]
(Caenorhabditis elegans)
IVD [mitochondrial matrix]
(Canis familiaris)
IVD [mitochondrial matrix]
(Danio rerio)
IVD [mitochondrial matrix]
(Dictyostelium discoideum)
IVD [mitochondrial matrix]
(Drosophila melanogaster)
IVD [mitochondrial matrix]
(Gallus gallus)
IVD [mitochondrial matrix]
(Mus musculus)
IVD [mitochondrial matrix]
(Rattus norvegicus)
IVD [mitochondrial matrix]
(Sus scrofa)
IVD [mitochondrial matrix]
(Xenopus tropicalis)
Cross References
RefSeq
NP_002216.2
,
NP_001152980.1
OpenTargets
ENSG00000128928
IntEnz
1.3.8.4
HPA
ENSG00000128928-IVD
GeneCards
P26440
Ensembl
ENSP00000499074
,
ENST00000651168
,
ENSG00000128928
,
ENST00000650656
,
ENSP00000498731
PRO
P26440
Pharos - Targets
P26440
Orphanet
16277
PDB
1IVH
HMDB Protein
HMDBP00166
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q15831 STK11
2
STK11 [cytosol]
(R-HSA-380954)
STK11 [nucleoplasm]
(R-HSA-164119)
0.527
2
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