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ub-CFTR F508del [cytosol]
Stable Identifier
R-HSA-8866844
Type
Complex
Species
Homo sapiens
Compartment
cytosol
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Disorders of transmembrane transporters (Homo sapiens)
ABC transporter disorders (Homo sapiens)
Defective CFTR causes cystic fibrosis (Homo sapiens)
CFTR F508del is degraded by the 26S proteasome (Homo sapiens)
ub-CFTR F508del [cytosol] (Homo sapiens)
VCP-catalyzed ATP hydrolysis promotes the translocation of CFTR F508del into the cytosol (Homo sapiens)
ub-CFTR F508del [cytosol] (Homo sapiens)
Participants
components
Ub [cytosol]
(Homo sapiens)
ub-CFTR F508del [cytosol]
(Homo sapiens)
Participates
as an input of
CFTR F508del is degraded by the 26S proteasome (Homo sapiens)
as an output of
VCP-catalyzed ATP hydrolysis promotes the translocation of CFTR F508del into the cytosol (Homo sapiens)
Disease
Name
Identifier
Synonyms
cystic fibrosis
DOID:1485
mucoviscidosis, CF
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