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COQ9 [mitochondrial inner membrane]
Stable Identifier
R-HSA-8932994
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
Ubiquinone biosynthesis protein COQ9, mitochondrial, COQ9_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of cofactors (Homo sapiens)
Ubiquinol biosynthesis (Homo sapiens)
COQ9 dimer:COQ7:Fe2+ hydroxylates DMQ10H2 to DeMQ10H2 (Homo sapiens)
COQ9 dimer:COQ7:Fe2+ [mitochondrial inner membrane] (Homo sapiens)
COQ9 dimer [mitochondrial inner membrane] (Homo sapiens)
COQ9 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O75208 COQ9
Gene Names
COQ9, C16orf49, HSPC326, PSEC0129
Chain
transit peptide:1-44, chain:45-318
Reference Genes
BioGPS Gene:57017 COQ9
COSMIC (genes):COQ9 COQ9
CTD Gene:57017 COQ9
dbSNP Gene:57017 COQ9
ENSEMBL:ENSG00000088682.14 COQ9
HGNC:25302 COQ9
KEGG Gene (Homo sapiens):57017 COQ9
Monarch:57017 COQ9
NCBI Gene:57017 COQ9
OMIM:612837 COQ9
UCSC:O75208 COQ9
Reference Transcript
RefSeq:NM_020312.3 COQ9
Other Identifiers
11718580_a_at
16819497
212228_PM_s_at
212228_s_at
34810_at
3662724
3662725
3662729
3662730
3662734
3662735
3662738
3662740
3662742
3662746
3662747
3662748
3662749
57017
76019_f_at
7996041
A_23_P14928
GO:0005515
GO:0005739
GO:0005743
GO:0006091
GO:0006120
GO:0006744
GO:0008289
GO:0042803
GO:0043226
GO:0110142
HMNXSV003001236
Hs.4288.1.S1_3p_a_at
ILMN_1756898
TC16000490.hg
Participates
as a component of
COQ9 dimer [mitochondrial inner membrane] (Homo sapiens)
Cross References
RefSeq
NP_064708.1
OpenTargets
ENSG00000088682
GeneCards
O75208
HPA
ENSG00000088682-COQ9
Ensembl
ENST00000262507
,
ENSP00000262507
,
ENSG00000088682
PRO
O75208
Pharos - Targets
O75208
Orphanet
18460
PDB
6AWL
,
4RHP
,
7SSS
,
6DEW
,
7SSP
Interactors (9)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q96CM8 ACSF2
1
ACSF2 [mitochondrial matrix]
(R-HSA-5696005)
0.666
4
UniProt:Q5HYK3 COQ5
1
COQ5 [mitochondrial matrix]
(R-HSA-2162210)
0.591
11
UniProt:P09601 HMOX1
4
HMOX1 [nucleoplasm]
(R-HSA-9708567)
HMOX1 [mitochondrial outer membrane]
(R-HSA-9708524)
HMOX1 [endoplasmic reticulum membrane]
(R-HSA-189395)
HMOX1 [cytosol]
(R-HSA-9609901)
0.556
3
UniProt:Q14162 SCARF1
2
SCARF1 [plasma membrane]
(R-HSA-2197636)
SCARF1 [endocytic vesicle membrane]
(R-HSA-2239453)
0.556
3
UniProt:Q08426 EHHADH
2
EHHADH [peroxisomal matrix]
(R-HSA-400155)
EHHADH [cytosol]
(R-HSA-9033147)
0.556
3
UniProt:Q15848 ADIPOQ
1
ADIPOQ [extracellular region]
(R-HSA-1183052)
0.556
3
UniProt:Q13277 STX3
1
STX3 [plasma membrane]
(R-HSA-449131)
0.556
3
UniProt:Q9HCL2 GPAM
1
GPAM(1-828) [mitochondrial outer membrane]
(R-HSA-61855)
0.499
2
UniProt:Q9NZJ6 COQ3
1
COQ3(?-369) [mitochondrial matrix]
(R-HSA-2162206)
0.499
6
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