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COQ9 [mitochondrial inner membrane]
Stable Identifier
R-HSA-8932994
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
Ubiquinone biosynthesis protein COQ9, mitochondrial, COQ9_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of cofactors (Homo sapiens)
Ubiquinol biosynthesis (Homo sapiens)
COQ3 methylates DHDB (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ3 methylates DeMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ5 methylates MDMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ6 hydroxylates DHB (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ8A,B:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ9 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O75208 COQ9
Gene Names
COQ9, C16orf49, HSPC326, PSEC0129
Chain
transit peptide:1-44, chain:45-318
Reference Genes
BioGPS Gene:57017 COQ9
COSMIC (genes):COQ9 COQ9
CTD Gene:57017 COQ9
dbSNP Gene:57017 COQ9
ENSEMBL:ENSG00000088682 COQ9
ENSEMBL_homo_sapiens_GENE:ENSG00000088682.14 COQ9
HGNC:25302 COQ9
KEGG Gene (Homo sapiens):57017 COQ9
Monarch:57017 COQ9
NCBI Gene:57017 COQ9
OMIM:612837 COQ9
UCSC:O75208 COQ9
Reference Transcript
RefSeq:NM_020312.3 COQ9
Other Identifiers
11718580_a_at
16819497
212228_PM_s_at
212228_s_at
34810_at
3662724
3662725
3662729
3662730
3662734
3662735
3662738
3662740
3662742
3662746
3662747
3662748
3662749
57017
76019_f_at
7996041
A_23_P14928
GO:0005515
GO:0005739
GO:0005743
GO:0006091
GO:0006120
GO:0006744
GO:0008289
GO:0042803
GO:0043226
GO:0110142
HMNXSV003001236
Hs.4288.1.S1_3p_a_at
ILMN_1756898
TC16000490.hg
Participates
as a component of
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
Inferred To
si:ch211-51l3.4 [mitochondrial inner membrane]
(Danio rerio)
Ghost homologue of COQ9 [mitochondrial inner membrane]
(Caenorhabditis elegans)
COQ9 [mitochondrial inner membrane]
(Bos taurus)
COQ9 [mitochondrial inner membrane]
(Canis familiaris)
COQ9 [mitochondrial inner membrane]
(Dictyostelium discoideum)
COQ9 [mitochondrial inner membrane]
(Drosophila melanogaster)
COQ9 [mitochondrial inner membrane]
(Gallus gallus)
COQ9 [mitochondrial inner membrane]
(Mus musculus)
COQ9 [mitochondrial inner membrane]
(Rattus norvegicus)
COQ9 [mitochondrial inner membrane]
(Saccharomyces cerevisiae)
COQ9 [mitochondrial inner membrane]
(Schizosaccharomyces pombe)
COQ9 [mitochondrial inner membrane]
(Sus scrofa)
COQ9 [mitochondrial inner membrane]
(Xenopus tropicalis)
Cross References
RefSeq
NP_064708.1
OpenTargets
ENSG00000088682
HPA
ENSG00000088682-COQ9
GeneCards
O75208
Ensembl
ENSP00000262507
,
ENSG00000088682
,
ENST00000262507
PRO
O75208
Pharos - Targets
O75208
Orphanet
18460
PDB
6DEW
,
4RHP
,
7SSS
,
7SSP
,
6AWL
Interactors (8)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q96CM8 ACSF2
1
ACSF2 [mitochondrial matrix]
(R-HSA-5696005)
0.666
4
UniProt:P09601 HMOX1
4
HMOX1 [nucleoplasm]
(R-HSA-9708567)
HMOX1 [mitochondrial outer membrane]
(R-HSA-9708524)
HMOX1 [endoplasmic reticulum membrane]
(R-HSA-189395)
HMOX1 [cytosol]
(R-HSA-9609901)
0.556
3
UniProt:Q08426 EHHADH
2
EHHADH [peroxisomal matrix]
(R-HSA-400155)
EHHADH [cytosol]
(R-HSA-9033147)
0.556
3
UniProt:Q13277 STX3
1
STX3 [plasma membrane]
(R-HSA-449131)
0.556
3
UniProt:Q15848 ADIPOQ
1
ADIPOQ [extracellular region]
(R-HSA-1183052)
0.556
3
UniProt:Q14508 WFDC2
1
WFDC2 [extracellular region]
(R-HSA-9830363)
0.556
3
UniProt:Q14162 SCARF1
2
SCARF1 [plasma membrane]
(R-HSA-2197636)
SCARF1 [endocytic vesicle membrane]
(R-HSA-2239453)
0.556
3
UniProt:Q9HCL2 GPAM
1
GPAM(1-828) [mitochondrial outer membrane]
(R-HSA-61855)
0.499
2
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