Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
Idh2 [mitochondrial matrix]
Stable Identifier
R-MMU-450988
Type
Protein [EntityWithAccessionedSequence]
Species
Mus musculus
Compartment
mitochondrial matrix
Synonyms
IDH2, P54071
Locations in the PathwayBrowser
Expand all
Metabolism (Mus musculus)
Aerobic respiration and respiratory electron transport (Mus musculus)
Citric acid cycle (TCA cycle) (Mus musculus)
IDH2 dimer decarboxylates isocitrate (Mus musculus)
IDH2 dimer [mitochondrial matrix] (Mus musculus)
Idh2 [mitochondrial matrix] (Mus musculus)
Maturation of TCA enzymes and regulation of TCA cycle (Mus musculus)
ACAT1 tetramer acetylates IDH2 dimer (Mus musculus)
IDH2 dimer [mitochondrial matrix] (Mus musculus)
Idh2 [mitochondrial matrix] (Mus musculus)
SIRT3 deacetylates AcK-IDH2 dimer (Mus musculus)
IDH2 dimer [mitochondrial matrix] (Mus musculus)
Idh2 [mitochondrial matrix] (Mus musculus)
Metabolism of proteins (Mus musculus)
Mitochondrial protein degradation (Mus musculus)
CLPXP binds mitochondrial matrix proteins (Mus musculus)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
Idh2 [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
Idh2 [mitochondrial matrix] (Mus musculus)
CLPXP degrades mitochondrial matrix proteins (Mus musculus)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
Idh2 [mitochondrial matrix] (Mus musculus)
Organelle biogenesis and maintenance (Mus musculus)
Mitochondrial biogenesis (Mus musculus)
Transcriptional activation of mitochondrial biogenesis (Mus musculus)
SIRT3 deacetylates ACCS2, GLUD, IDH2, SOD2 (Mus musculus)
ACCS2,GLUD,IDH2,SOD2 [mitochondrial matrix] (Mus musculus)
Idh2 [mitochondrial matrix] (Mus musculus)
External Reference Information
External Reference
UniProt:P54071
Gene Names
Idh2
Reference Genes
BioGPS Gene:269951 Idh2
ENSEMBL:ENSMUSG00000030541
KEGG:mmu:269951 Idh2
Monarch:269951 Idh2
NCBI Gene:269951 Idh2
UCSC:P54071 Idh2
Reference Transcript
RefSeq:NM_173011.2 Idh2
Other Identifiers
10564857
1450048_a_at
17492478
269951
4332889
4458650
4485604
4696094
4806296
4818311
4826171
4922968
5152438
5199251
5253632
5303076
5340015
5430946
5457683
5482919
5488399
5535388
5585192
95693_at
A_55_P2118684
GE34612
GO:0000287
GO:0004450
GO:0005739
GO:0005743
GO:0005777
GO:0005829
GO:0005975
GO:0006097
GO:0006099
GO:0006102
GO:0006103
GO:0006739
GO:0006741
GO:0016491
GO:0016616
GO:0046872
GO:0051287
GO:0055086
GO:0060253
GO:1903976
GO:1904465
ILMN_2595612
U51167_s_at
mMC011820
Participates
as a member of
ACCS2,GLUD,IDH2,SOD2 [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
as a component of
IDH2 dimer [mitochondrial matrix] (Mus musculus)
Other forms of this molecule
Idh2 [mitochondrial matrix]
Inferred From
IDH2 [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_766599.2
ENSEMBL
ENSMUSP00000103007
,
ENSMUST00000107384
,
ENSMUSG00000030541
PRO
P54071
GlyGen
P54071
MGI
96414
PDB
5H3F
,
5H3E
© 2026
Reactome
This website requires cookies and the limited processing of your personal data in order to function. By using the site you are agreeing to this as outlined in our
Privacy Notice
.
I agree, dismiss this banner
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text