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ECHS1 [mitochondrial matrix]
Stable Identifier
R-MMU-54125
Type
Protein [EntityWithAccessionedSequence]
Species
Mus musculus
Compartment
mitochondrial matrix
Synonyms
Q8BH95
Locations in the PathwayBrowser
Expand all
Metabolism (Mus musculus)
Metabolism of amino acids and derivatives (Mus musculus)
Branched-chain amino acid catabolism (Mus musculus)
ECHS1 hydrates methacrylyl-CoA (Mus musculus)
ECHS1 [mitochondrial matrix] (Mus musculus)
ECHS1 hexamer [mitochondrial matrix] (Mus musculus)
ECHS1 [mitochondrial matrix] (Mus musculus)
Metabolism of lipids (Mus musculus)
Fatty acid metabolism (Mus musculus)
Mitochondrial Fatty Acid Beta-Oxidation (Mus musculus)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Mus musculus)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Mus musculus)
Crotonoyl-CoA+H2O<=>(S)-3-Hydroxybutanoyl-CoA (Mus musculus)
ECHS1 [mitochondrial matrix] (Mus musculus)
ECHS1 hexamer [mitochondrial matrix] (Mus musculus)
ECHS1 [mitochondrial matrix] (Mus musculus)
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Mus musculus)
trans-Dec-2-enoyl-CoA+H2O<=>(S)-Hydroxydecanoyl-CoA (Mus musculus)
ECHS1 [mitochondrial matrix] (Mus musculus)
ECHS1 hexamer [mitochondrial matrix] (Mus musculus)
ECHS1 [mitochondrial matrix] (Mus musculus)
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Mus musculus)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Mus musculus)
ECHS1 [mitochondrial matrix] (Mus musculus)
ECHS1 hexamer [mitochondrial matrix] (Mus musculus)
ECHS1 [mitochondrial matrix] (Mus musculus)
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Mus musculus)
2-trans-Dodecenoyl-CoA+H2O<=>(S)-3-Hydroxydodecanoyl-CoA (Mus musculus)
ECHS1 [mitochondrial matrix] (Mus musculus)
ECHS1 hexamer [mitochondrial matrix] (Mus musculus)
ECHS1 [mitochondrial matrix] (Mus musculus)
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Mus musculus)
trans-Oct-2-enoyl-CoA+H2O<=>(S)-Hydroxyoctanoyl-CoA (Mus musculus)
ECHS1 [mitochondrial matrix] (Mus musculus)
ECHS1 hexamer [mitochondrial matrix] (Mus musculus)
ECHS1 [mitochondrial matrix] (Mus musculus)
External Reference Information
External Reference
UniProt:Q8BH95
Reference Genes
BioGPS Gene:93747
ENSEMBL:ENSMUSG00000025465
ENSEMBL:ENSMUSG00000025465.14
KEGG Gene (Mus musculus):93747
Monarch:93747
NCBI Gene:93747
UCSC:Q8BH95
Reference Transcript
RefSeq:NM_053119.2
Other Identifiers
10568939
1452341_at
17497612
4324673
4424295
4454204
4516657
4624356
4700658
4740007
5096274
5251014
5307584
5328067
5441718
93747
95426_at
A_51_P409039
A_66_P127621
GE38273
GO:0003824
GO:0004165
GO:0004300
GO:0005739
GO:0005759
GO:0006629
GO:0006631
GO:0006635
GO:0016829
GO:0016853
GO:0043226
GO:0043956
GO:0120092
ILMN_2719222
ILMN_2888181
aa270965_s_at
mMC010583
Participates
as a component of
ECHS1 hexamer [mitochondrial matrix] (Mus musculus)
Inferred From
ECHS1 [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_444349.1
IntEnz
5.3.3.8
Ensembl
ENSMUSP00000026538
,
ENSMUSG00000025465
,
ENSMUST00000026538
PRO
Q8BH95
MGI
2136460
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