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Ndufa1 [mitochondrial inner membrane]
Stable Identifier
R-MMU-60212
Type
Protein [EntityWithAccessionedSequence]
Species
Mus musculus
Compartment
mitochondrial inner membrane
Synonyms
NDUFA1, O35683
Locations in the PathwayBrowser
Expand all
Metabolism (Mus musculus)
Aerobic respiration and respiratory electron transport (Mus musculus)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Mus musculus)
Respiratory electron transport (Mus musculus)
Complex I biogenesis (Mus musculus)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa1 [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa1 [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa1 [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa1 [mitochondrial inner membrane] (Mus musculus)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa1 [mitochondrial inner membrane] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa1 [mitochondrial inner membrane] (Mus musculus)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa1 [mitochondrial inner membrane] (Mus musculus)
980kDa complex [mitochondrial inner membrane] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa1 [mitochondrial inner membrane] (Mus musculus)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa1 [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa1 [mitochondrial inner membrane] (Mus musculus)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Mus musculus)
980kDa complex [mitochondrial inner membrane] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa1 [mitochondrial inner membrane] (Mus musculus)
Complex I [mitochondrial inner membrane] (Mus musculus)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa1 [mitochondrial inner membrane] (Mus musculus)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Mus musculus)
Complex I [mitochondrial inner membrane] (Mus musculus)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa1 [mitochondrial inner membrane] (Mus musculus)
External Reference Information
External Reference
UniProt:O35683
Gene Names
Ndufa1
Reference Genes
BioGPS Gene:54405 Ndufa1
ENSEMBL:ENSMUSG00000016427
ENSEMBL:ENSMUSG00000016427.8 Ndufa1
KEGG Gene (Mus musculus):54405 Ndufa1
Monarch:54405 Ndufa1
NCBI Gene:54405 Ndufa1
UCSC:O35683 Ndufa1
Reference Transcript
RefSeq:NM_019443.2 Ndufa1
Other Identifiers
10604100
1422241_a_at
17541036
4519313
5222293
5349452
54405
5597249
A_51_P472405
A_52_P139747
GE37398
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0007005
GO:0009060
GO:0016020
GO:0031966
GO:0032981
GO:0042776
GO:0043226
GO:0055086
GO:0065003
GO:0070469
GO:1901135
ILMN_1251370
Y07708_s_at
mMC002673
Participates
as a component of
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Inferred From
NDUFA1 [mitochondrial inner membrane]
(Homo sapiens)
Cross References
RefSeq
NP_062316.1
Ensembl
ENSMUSG00000016427
,
ENSMUSP00000016571
,
ENSMUST00000016571
PRO
O35683
MGI
1929511
PDB
6ZTQ
,
7AK6
,
6ZR2
,
6G72
,
7B93
,
6G2J
,
8OM1
,
7AK5
,
7PSA
,
8OLT
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