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ECHS1 [mitochondrial matrix]
Stable Identifier
R-RNO-54125
Type
Protein [EntityWithAccessionedSequence]
Species
Rattus norvegicus
Compartment
mitochondrial matrix
Synonyms
P14604
Locations in the PathwayBrowser
Expand all
Metabolism (Rattus norvegicus)
Metabolism of amino acids and derivatives (Rattus norvegicus)
Branched-chain amino acid catabolism (Rattus norvegicus)
ECHS1 hydrates methacrylyl-CoA (Rattus norvegicus)
ECHS1 [mitochondrial matrix] (Rattus norvegicus)
ECHS1 hexamer [mitochondrial matrix] (Rattus norvegicus)
ECHS1 [mitochondrial matrix] (Rattus norvegicus)
Metabolism of lipids (Rattus norvegicus)
Fatty acid metabolism (Rattus norvegicus)
Mitochondrial Fatty Acid Beta-Oxidation (Rattus norvegicus)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Rattus norvegicus)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Rattus norvegicus)
Crotonoyl-CoA+H2O => (S)-3-Hydroxybutanoyl-CoA (Rattus norvegicus)
ECHS1 [mitochondrial matrix] (Rattus norvegicus)
ECHS1 hexamer [mitochondrial matrix] (Rattus norvegicus)
ECHS1 [mitochondrial matrix] (Rattus norvegicus)
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Rattus norvegicus)
trans-Dec-2-enoyl-CoA+H2O => (S)-Hydroxydecanoyl-CoA (Rattus norvegicus)
ECHS1 [mitochondrial matrix] (Rattus norvegicus)
ECHS1 hexamer [mitochondrial matrix] (Rattus norvegicus)
ECHS1 [mitochondrial matrix] (Rattus norvegicus)
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Rattus norvegicus)
trans-Hex-2-enoyl-CoA+H2O<=>(S)-Hydroxyhexanoyl-CoA (Rattus norvegicus)
ECHS1 [mitochondrial matrix] (Rattus norvegicus)
ECHS1 hexamer [mitochondrial matrix] (Rattus norvegicus)
ECHS1 [mitochondrial matrix] (Rattus norvegicus)
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Rattus norvegicus)
2-trans-Dodecenoyl-CoA+H2O =>( S)-3-Hydroxydodecanoyl-CoA (Rattus norvegicus)
ECHS1 [mitochondrial matrix] (Rattus norvegicus)
ECHS1 hexamer [mitochondrial matrix] (Rattus norvegicus)
ECHS1 [mitochondrial matrix] (Rattus norvegicus)
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Rattus norvegicus)
trans-Oct-2-enoyl-CoA+H2O => (S)-Hydroxyoctanoyl-CoA (Rattus norvegicus)
ECHS1 [mitochondrial matrix] (Rattus norvegicus)
ECHS1 hexamer [mitochondrial matrix] (Rattus norvegicus)
ECHS1 [mitochondrial matrix] (Rattus norvegicus)
External Reference Information
External Reference
UniProt:P14604
Reference Genes
BioGPS Gene:140547
ENSEMBL:ENSRNOG00000018522
ENSEMBL:ENSRNOG00000047565
ENSEMBL:ENSRNOG00000064647
ENSEMBL:ENSRNOG00055027621
ENSEMBL:ENSRNOG00060025390
ENSEMBL:ENSRNOG00065017885
KEGG:rno:140547
Monarch:140547
NCBI Gene:140547
UCSC:P14604
Reference Transcript
RefSeq:NM_078623.2
Other Identifiers
10726611
1367829_at
140547
17638151
5674343
5682948
5707493
5726912
5781076
6052654
6186090
6376575
6384662
6430571
A_43_P13066
GE21094
GO:0003824
GO:0004300
GO:0005739
GO:0006629
GO:0006635
ILMN_1373267
PH_rn_0011674
X15958_at
Participates
as a component of
ECHS1 hexamer [mitochondrial matrix] (Rattus norvegicus)
Inferred From
ECHS1 [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_511178.1
ENSEMBL
ENSRNOT00000071574
,
ENSRNOP00000066388
,
ENSRNOG00000064647
ZINC - Substances
ECHM_RAT
ZINC target
P14604
PRO
P14604
GlyGen
P14604
RGD
69330
PDB
1MJ3
,
1DUB
,
1EY3
,
2DUB
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