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NFS1 [mitochondrial matrix]
Stable Identifier
R-SSC-1362396
Type
Protein [EntityWithAccessionedSequence]
Species
Sus scrofa
Compartment
mitochondrial matrix
Synonyms
PXLP-K258-NFS1-1, B6UV57
Locations in the PathwayBrowser
Expand all
Metabolism (Sus scrofa)
Aerobic respiration and respiratory electron transport (Sus scrofa)
Citric acid cycle (TCA cycle) (Sus scrofa)
Maturation of TCA enzymes and regulation of TCA cycle (Sus scrofa)
Transfer of Fe-S clusters to SDHB (Sus scrofa)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Sus scrofa)
NFS1 [mitochondrial matrix] (Sus scrofa)
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Sus scrofa)
NFS1 [mitochondrial matrix] (Sus scrofa)
Respiratory electron transport (Sus scrofa)
Complex III assembly (Sus scrofa)
2Fe-2S is inserted in UQCRFS1 (Sus scrofa)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Sus scrofa)
NFS1 [mitochondrial matrix] (Sus scrofa)
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Sus scrofa)
NFS1 [mitochondrial matrix] (Sus scrofa)
Mitochondrial iron-sulfur cluster biogenesis (Sus scrofa)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Sus scrofa)
2 Iron:FXN:NFS1:ISD11:ISCU [mitochondrial matrix] (Sus scrofa)
NFS1 [mitochondrial matrix] (Sus scrofa)
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Sus scrofa)
NFS1 [mitochondrial matrix] (Sus scrofa)
NFS1 [mitochondrial matrix] (Sus scrofa)
Frataxin binds iron (Sus scrofa)
2 Iron:FXN:NFS1:ISD11:ISCU [mitochondrial matrix] (Sus scrofa)
NFS1 [mitochondrial matrix] (Sus scrofa)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Sus scrofa)
NFS1 [mitochondrial matrix] (Sus scrofa)
External Reference Information
External Reference
UniProt:B6UV57
Gene Names
NFS1
Reference Genes
BioGPS Gene:100156145 NFS1
ENSEMBL:ENSSSCG00000007307.5
KEGG:ssc:100156145 NFS1
Monarch:100156145 NFS1
NCBI Gene:100156145 NFS1
UCSC:B6UV57 NFS1
Reference Transcript
RefSeq:NM_001136510.1 NFS1
Other Identifiers
100156145
GO:0003824
GO:0005634
GO:0005654
GO:0005737
GO:0005739
GO:0005759
GO:0005813
GO:0005815
GO:0005829
GO:0005856
GO:0006790
GO:0016226
GO:0016740
GO:0030170
GO:0031071
GO:0042803
GO:0043226
GO:0044571
GO:0044572
GO:0046872
GO:0051536
GO:0099128
Ssc.4969.1.S1_at
Participates
as a component of
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Sus scrofa)
2 Iron:FXN:NFS1:ISD11:ISCU [mitochondrial matrix] (Sus scrofa)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Sus scrofa)
Other forms of this molecule
NFS1 [cytosol]
Inferred From
PXLP-K258-NFS1-1 [mitochondrial matrix]
(Homo sapiens)
Modified Residues
Name
N6-pyridoxal phosphate-L-lysine at 258 (in Homo sapiens)
Coordinate
258
PsiMod Name
N6-pyridoxal phosphate-L-lysine [MOD:00128]
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to N6-pyridoxal phosphate-L-lysine.
Cross References
RefSeq
NP_001129982.1
ENSEMBL
ENSSSCP00000007781
,
ENSSSCG00000007307
,
ENSSSCT00000007995
VGNC
99724
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