Search results for ALDH5A1

Showing 3 results out of 3

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Species

Types

Compartments

Reaction types

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Protein (1 results from a total of 1)

Identifier: R-HSA-916831
Species: Homo sapiens
Compartment: mitochondrial matrix
Primary external reference: UniProt: ALDH5A1: P51649

Complex (1 results from a total of 1)

Identifier: R-HSA-9653545
Species: Homo sapiens
Compartment: mitochondrial matrix

Reaction (1 results from a total of 1)

Identifier: R-HSA-888548
Species: Homo sapiens
Compartment: mitochondrial matrix
Mitochondrial succinate semialdehyde dehydrogenase (ALDH5A1) tetramer catalyzes the reaction of succinate semialdehyde (SUCCSA), H2O, and NAD+ to form succinate (SUCCA) and NADH + 2 H+ (Kim et al. 2009). Mutations that inactivate this gene cause 4-hydroxybutyric aciduria (succinic semialdehyde dehydrogenase deficiency) (Chambliss et al. 1998).
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