Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
BEST3 [plasma membrane]
Stable Identifier
R-HSA-2744362
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
plasma membrane
Synonyms
Bestrophin-3, BEST3_HUMAN
Locations in the PathwayBrowser
Expand all
Transport of small molecules (Homo sapiens)
Ion channel transport (Homo sapiens)
Stimuli-sensing channels (Homo sapiens)
BESTs transport cytosolic Cl- to extracellular region (Homo sapiens)
BESTs [plasma membrane] (Homo sapiens)
BEST3 [plasma membrane] (Homo sapiens)
BESTs transport cytosolic HCO3- to extracellular region (Homo sapiens)
BESTs [plasma membrane] (Homo sapiens)
BEST3 [plasma membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q8N1M1 BEST3
Gene Names
BEST3, VMD2L3
Chain
chain:1-668
Reference Genes
BioGPS Gene:144453 BEST3
COSMIC - genes:BEST3 BEST3
CTD Gene:144453 BEST3
dbSNP Gene:144453 BEST3
ENSEMBL:ENSG00000127325 BEST3
HGNC:17105 BEST3
KEGG:hsa:144453 BEST3
Monarch:144453 BEST3
NCBI Gene:144453 BEST3
OMIM:607337 BEST3
UCSC:Q8N1M1 BEST3
Reference Transcript
RefSeq:XM_047428376.1 BEST3
RefSeq:XM_011537961.2 BEST3
RefSeq:NM_152439.4 BEST3
RefSeq:XM_054371185.1 BEST3
RefSeq:NM_001282613.2 BEST3
RefSeq:NM_032735.3 BEST3
RefSeq:XM_054371184.1 BEST3
RefSeq:XM_047428383.1 BEST3
RefSeq:NM_001282615.2 BEST3
RefSeq:NM_001282616.2 BEST3
RefSeq:NM_001282614.2 BEST3
Other Identifiers
11731382_a_at
11759676_at
11762735_a_at
144453
1555492_PM_a_at
1555492_a_at
16767373
224520_PM_s_at
224520_s_at
237003_PM_at
237003_at
3461500
3461501
3461503
3461504
3461505
3461506
3461507
3461511
3461512
3461513
3461514
3461516
3461517
3461518
3461519
3461523
3461524
3461525
3461527
3461530
3461531
3461534
3461535
3461536
3461537
3461538
3461539
3461540
76431_at
78111_i_at
78113_r_at
7964852
81849_at
90332_at
A_23_P323801
A_33_P3249877
A_33_P3249888
GE477297
GE83500
GO:0005229
GO:0005254
GO:0005515
GO:0005886
GO:0006811
GO:0006821
GO:0015267
GO:0015698
GO:0016020
GO:0034220
GO:0034707
GO:0043271
GO:0046872
GO:0055085
GO:0099095
GO:1902476
HMNXSV003012541
HMNXSV003025414
HMNXSV003029889
HMNXSV003033775
Hs.125296.0.A1_3p_at
Hs2.122128.2.S1_3p_at
ILMN_1720600
ILMN_1790794
ILMN_2410182
PH_hs_0006826
PH_hs_0024901
TC12001712.hg
g13623640_3p_s_at
Participates
as a candidate of
BESTs [plasma membrane] (Homo sapiens)
Inferred To
best-22 [plasma membrane]
(Caenorhabditis elegans)
best-2 [plasma membrane]
(Caenorhabditis elegans)
best-8 [plasma membrane]
(Caenorhabditis elegans)
best-5 [plasma membrane]
(Caenorhabditis elegans)
BEST3 [plasma membrane]
(Bos taurus)
BEST3 [plasma membrane]
(Caenorhabditis elegans)
BEST3 [plasma membrane]
(Canis familiaris)
BEST3 [plasma membrane]
(Gallus gallus)
BEST3 [plasma membrane]
(Mus musculus)
BEST3 [plasma membrane]
(Sus scrofa)
Best2 [plasma membrane]
(Drosophila melanogaster)
best-15 [plasma membrane]
(Caenorhabditis elegans)
best-18 [plasma membrane]
(Caenorhabditis elegans)
best-25 [plasma membrane]
(Caenorhabditis elegans)
best3 [plasma membrane]
(Xenopus tropicalis)
best-12 [plasma membrane]
(Caenorhabditis elegans)
best-21 [plasma membrane]
(Caenorhabditis elegans)
Homologues of BEST3 [plasma membrane]
(Caenorhabditis elegans)
Homologues of BEST3 [plasma membrane]
(Drosophila melanogaster)
best-6 [plasma membrane]
(Caenorhabditis elegans)
best-16 [plasma membrane]
(Caenorhabditis elegans)
best-26 [plasma membrane]
(Caenorhabditis elegans)
Best3 [plasma membrane]
(Drosophila melanogaster)
Best3 [plasma membrane]
(Rattus norvegicus)
best-3 [plasma membrane]
(Caenorhabditis elegans)
best-19 [plasma membrane]
(Caenorhabditis elegans)
best-14 [plasma membrane]
(Caenorhabditis elegans)
best-11 [plasma membrane]
(Caenorhabditis elegans)
best-17 [plasma membrane]
(Caenorhabditis elegans)
Best4 [plasma membrane]
(Drosophila melanogaster)
best-20 [plasma membrane]
(Caenorhabditis elegans)
best-10 [plasma membrane]
(Caenorhabditis elegans)
Best1 [plasma membrane]
(Drosophila melanogaster)
best-24 [plasma membrane]
(Caenorhabditis elegans)
best-4 [plasma membrane]
(Caenorhabditis elegans)
best-7 [plasma membrane]
(Caenorhabditis elegans)
Cross References
RefSeq
XP_011536263.1
,
XP_054227160.1
,
XP_047284332.1
,
NP_001269543.1
,
NP_689652.2
,
NP_116124.2
,
NP_001269544.1
,
XP_054227159.1
,
XP_047284339.1
,
NP_001269542.1
,
NP_001269545.1
OpenTargets
ENSG00000127325
ENSEMBL
ENSP00000332413
,
ENSP00000266661
,
ENSP00000329064
,
ENST00000266661
,
ENSP00000449548
,
ENSP00000449377
,
ENSG00000127325
,
ENST00000551160
,
ENSP00000433213
,
ENST00000553096
,
ENST00000330891
,
ENST00000331471
,
ENST00000488961
HPA
ENSG00000127325-BEST3
GeneCards
BEST3
PRO
Q8N1M1
Pharos - Targets
Q8N1M1
HMDB Protein
HMDBP07426
© 2026
Reactome
This website requires cookies and the limited processing of your personal data in order to function. By using the site you are agreeing to this as outlined in our
Privacy Notice
.
I agree, dismiss this banner
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text