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ATP5L [mitochondrial inner membrane]
Stable Identifier
R-HSA-50518
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
ATP synthase g chain, mitochondrial , ATPase subunit G
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Formation of ATP by chemiosmotic coupling (Homo sapiens)
ADP and Pi bind to ATPase (Homo sapiens)
ATPase:ADP:Pi [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
ATP5L [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
ATP5L [mitochondrial inner membrane] (Homo sapiens)
ATPase synthesizes ATP (Homo sapiens)
ATPase:ADP:Pi [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
ATP5L [mitochondrial inner membrane] (Homo sapiens)
ATPase:ATP [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
ATP5L [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
ATP5L [mitochondrial inner membrane] (Homo sapiens)
Enzyme-bound ATP is released (Homo sapiens)
ATPase:ATP [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
ATP5L [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
ATP5L [mitochondrial inner membrane] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Mitochondrial protein degradation (Homo sapiens)
LONP1 binds mitochondrial inner membrane proteins (Homo sapiens)
LONP1:substrate protein (mitochondrial inner membrane) [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
ATP5L [mitochondrial inner membrane] (Homo sapiens)
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
ATP5L [mitochondrial inner membrane] (Homo sapiens)
LONP1 degrades mitochondrial inner membrane proteins (Homo sapiens)
LONP1:substrate protein (mitochondrial inner membrane) [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
ATP5L [mitochondrial inner membrane] (Homo sapiens)
Organelle biogenesis and maintenance (Homo sapiens)
Mitochondrial biogenesis (Homo sapiens)
Cristae formation (Homo sapiens)
F1Fo ATP synthase dimerizes (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
ATP5L [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase dimer [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
ATP5L [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O75964 ATP5MG
Gene Names
ATP5MG, ATP5L
Chain
initiator methionine:, chain:2-103
Reference Genes
BioGPS Gene:10632 ATP5MG
COSMIC (genes):ATP5MG ATP5MG
CTD Gene:10632 ATP5MG
dbSNP Gene:10632 ATP5MG
ENSEMBL:ENSG00000167283 ATP5L
ENSEMBL_homo_sapiens_GENE:ENSG00000167283.9 ATP5MG
HGNC:14247 ATP5MG
KEGG Gene (Homo sapiens):10632 ATP5MG
Monarch:10632 ATP5MG
NCBI Gene:10632 ATP5MG
OMIM:617473 ATP5MG
UCSC:O75964 ATP5MG
Reference Transcript
RefSeq:NM_006476.4 ATP5MG
Other Identifiers
10632
11721238_s_at
11721239_x_at
11757636_x_at
207573_PM_x_at
207573_x_at
208745_PM_at
208745_at
208746_PM_x_at
208746_x_at
210453_PM_x_at
210453_x_at
3351361
3351367
3351368
3351371
3351372
3351373
38693_at
7944216
A_23_P75622
A_24_P96527
GE56285
GE85997
GO:0000276
GO:0003824
GO:0005215
GO:0005515
GO:0005739
GO:0005743
GO:0005753
GO:0006091
GO:0006754
GO:0006811
GO:0015078
GO:0015986
GO:0016020
GO:0016874
GO:0042776
GO:0043226
GO:0045263
GO:0046933
GO:0055085
GO:0055086
GO:1901135
GO:1902600
HMNXSV003019965
Hs.107476.1.S2_3p_at
ILMN_1812638
ILMN_2079285
PH_hs_0005969
TC11002898.hg
g4454685_3p_x_at
g5453560_3p_a_at
Participates
as a member of
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
as a component of
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
Inferred To
ATP20 [mitochondrial inner membrane]
(Saccharomyces cerevisiae)
ATP5MG [mitochondrial inner membrane]
(Bos taurus)
ATP5MG [mitochondrial inner membrane]
(Canis familiaris)
Atp5mg [mitochondrial inner membrane]
(Mus musculus)
Atp5mg [mitochondrial inner membrane]
(Rattus norvegicus)
asg-2 [mitochondrial inner membrane]
(Caenorhabditis elegans)
ATPsynG [mitochondrial inner membrane]
(Drosophila melanogaster)
mg:bb02g11 [mitochondrial inner membrane]
(Danio rerio)
ATP5L [mitochondrial inner membrane]
(Gallus gallus)
ATP5L [mitochondrial inner membrane]
(Sus scrofa)
Cross References
RefSeq
NP_006467.4
OpenTargets
ENSG00000167283
HPA
ENSG00000167283-ATP5MG
GeneCards
O75964
Ensembl
ENSG00000167283
,
ENSP00000300688
,
ENST00000300688
PRO
O75964
Pharos - Targets
O75964
PDB
8H9U
,
8H9S
,
8H9Q
,
8H9T
,
8H9F
,
8H9M
,
8H9V
,
8H9J
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P13569 CFTR
17
PolyUb-CFTR [clathrin-coated endocytic vesicle membrane]
(R-HSA-8869104)
PolyUb-CFTR [plasma membrane]
(R-HSA-8867595)
CFTR [lysosomal membrane]
(R-HSA-5627279)
CFTR [Golgi-associated vesicle membrane]
(R-HSA-5627079)
CFTR [endosome membrane]
(R-HSA-6782965)
PolyUb-CFTR [endosome membrane]
(R-HSA-6782976)
CFTR F508del [endoplasmic reticulum membrane]
(R-HSA-8866834)
ub-CFTR F508del [cytosol]
(R-HSA-8866838)
ub-CFTR F508del [endoplasmic reticulum membrane]
(R-HSA-8866842)
CFTR G542* [plasma membrane]
(R-HSA-5678986)
CFTR G551D [plasma membrane]
(R-HSA-5678977)
CFTR W1282* [plasma membrane]
(R-HSA-5678976)
CFTR F508del [plasma membrane]
(R-HSA-5678978)
CFTR N1303K [plasma membrane]
(R-HSA-5678983)
CFTR [plasma membrane]
(R-HSA-383188)
CFTR [endoplasmic reticulum membrane]
(R-HSA-8866837)
misfolded CFTR [endoplasmic reticulum membrane]
(R-HSA-8868730)
0.483
7
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