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NDUFA9 [mitochondrial matrix]
Stable Identifier
R-HSA-163942
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
NADH-ubiquinone oxidoreductase 39 kDa subunit
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
The citric acid (TCA) cycle and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
IP subcomplex binds NDUFAF3, NDUFAF4, TIMMDC1 to form Intermediate 1 (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
NDUF subunits bind to form the IP subcomplex (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q16795 NDUFA9
Gene Names
NDUFA9, NDUFS2L
Chain
transit peptide:1-35, chain:36-377
Reference Genes
BioGPS Gene:4704 NDUFA9
COSMIC (genes):NDUFA9 NDUFA9
CTD Gene:4704 NDUFA9
dbSNP Gene:4704 NDUFA9
ENSEMBL:ENSG00000139180 NDUFA9
ENSEMBL_homo_sapiens_GENE:ENSG00000139180.11 NDUFA9
HGNC:7693 NDUFA9
KEGG Gene (Homo sapiens):4704 NDUFA9
Monarch:4704 NDUFA9
NCBI Gene:4704 NDUFA9
OMIM:603834 NDUFA9
UCSC:Q16795 NDUFA9
Reference Transcript
RefSeq:NM_005002.4 NDUFA9
Other Identifiers
11757029_a_at
16747077
208969_PM_at
208969_at
242620_PM_at
242620_at
3401879
3401882
3401883
3401884
3401887
3401888
3401889
3401891
3401892
3401894
3401898
3401900
3401901
3401902
3401903
3401906
3401908
3401910
3401912
3401913
3401915
3401917
36205_at
3959298
3959304
3959305
4704
51307_at
73284_at
7953243
86078_at
A_19_P00322045
A_19_P00810426
A_23_P76499
A_24_P361006
GE532274
GE61359
GE822567
GO:0003824
GO:0003954
GO:0005215
GO:0005515
GO:0005634
GO:0005739
GO:0005747
GO:0005759
GO:0006091
GO:0006120
GO:0006814
GO:0007005
GO:0007623
GO:0008137
GO:0009060
GO:0016491
GO:0031966
GO:0032981
GO:0042776
GO:0043226
GO:0044877
GO:0055086
GO:0065003
GO:0070469
GO:1901006
GO:1901135
HMNXSV003016368
Hs.269074.0.A1_3p_at
ILMN_1760741
L04490_at
PH_hs_0004290
PH_hs_0010136
TC12003205.hg
g5326822_3p_at
Participates
as a component of
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
Inferred To
ND-39 [mitochondrial matrix]
(Drosophila melanogaster)
NDUFA9 [mitochondrial matrix]
(Bos taurus)
NDUFA9 [mitochondrial matrix]
(Canis familiaris)
NDUFA9 [mitochondrial matrix]
(Gallus gallus)
NDUFA9 [mitochondrial matrix]
(Sus scrofa)
ndufa9 [mitochondrial matrix]
(Dictyostelium discoideum)
ndufa9 [mitochondrial matrix]
(Xenopus tropicalis)
nduf-9 [mitochondrial matrix]
(Caenorhabditis elegans)
Ghost homologue of NDUFA9 [mitochondrial matrix]
(Danio rerio)
Ndufa9 [mitochondrial matrix]
(Mus musculus)
Ndufa9 [mitochondrial matrix]
(Rattus norvegicus)
Cross References
RefSeq
NP_004993.1
OpenTargets
ENSG00000139180
HPA
ENSG00000139180-NDUFA9
GeneCards
Q16795
Ensembl
ENSP00000266544
,
ENSG00000139180
,
ENST00000266544
PRO
Q16795
Pharos - Targets
Q16795
Orphanet
20788
HMDB Protein
HMDBP00177
PDB
5XTI
,
5XTH
,
5XTB
,
5XTD
Interactors (5)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.725
8
UniProt:P42858 HTT
1
HTT [nucleoplasm]
(R-HSA-9023590)
0.666
7
UniProt:P19404 NDUFV2
1
NDUFV2 [mitochondrial inner membrane]
(R-HSA-163939)
0.564
3
UniProt:O75380 NDUFS6
1
NDUFS6 [mitochondrial inner membrane]
(R-HSA-163922)
0.527
3
UniProt:P78537 BLOC1S1
2
BLOC1S1 [Golgi membrane]
(R-HSA-434324)
BLOC1S1 [lysosomal membrane]
(R-HSA-429821)
0.524
3
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