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NDUFA9 [mitochondrial matrix]
Stable Identifier
R-HSA-163942
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
NADH-ubiquinone oxidoreductase 39 kDa subunit
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
IP subcomplex binds NDUFAF3, NDUFAF4, TIMMDC1 to form Intermediate 1 (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
NDUF subunits bind to form the IP subcomplex (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
NDUFA9 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q16795 NDUFA9
Gene Names
NDUFA9, NDUFS2L
Chain
transit peptide:1-35, chain:36-377
Reference Genes
BioGPS Gene:4704 NDUFA9
COSMIC (genes):NDUFA9 NDUFA9
CTD Gene:4704 NDUFA9
dbSNP Gene:4704 NDUFA9
ENSEMBL:ENSG00000139180 NDUFA9
HGNC:7693 NDUFA9
KEGG:hsa:4704 NDUFA9
Monarch:4704 NDUFA9
NCBI Gene:4704 NDUFA9
OMIM:603834 NDUFA9
UCSC:Q16795 NDUFA9
Reference Transcript
RefSeq:NM_005002.4 NDUFA9
Other Identifiers
11757029_a_at
16747077
208969_PM_at
208969_at
242620_PM_at
242620_at
3401879
3401881
3401882
3401883
3401884
3401885
3401886
3401887
3401888
3401889
3401891
3401892
3401894
3401895
3401897
3401898
3401900
3401901
3401902
3401903
3401906
3401908
3401910
3401912
3401913
3401915
3401917
36205_at
3959298
3959304
3959305
4704
51307_at
72458_at
73284_at
7953243
86078_at
A_19_P00322045
A_19_P00810426
A_23_P76499
A_24_P361006
GE532274
GE61359
GE822567
GO:0003824
GO:0003954
GO:0005215
GO:0005515
GO:0005634
GO:0005739
GO:0005743
GO:0005759
GO:0006091
GO:0006120
GO:0006814
GO:0007623
GO:0008137
GO:0009060
GO:0016491
GO:0031966
GO:0032981
GO:0042776
GO:0043226
GO:0044877
GO:0045271
GO:0055085
GO:0055086
GO:0065003
GO:1901006
GO:1901135
GO:1902600
HMNXSV003016368
Hs.269074.0.A1_3p_at
ILMN_1760741
L04490_at
PH_hs_0004290
PH_hs_0010136
TC12003205.hg
g5326822_3p_at
Participates
as a component of
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
Inferred To
ND-39 [mitochondrial matrix]
(Drosophila melanogaster)
NDUFA9 [mitochondrial matrix]
(Bos taurus)
NDUFA9 [mitochondrial matrix]
(Canis familiaris)
NDUFA9 [mitochondrial matrix]
(Gallus gallus)
NDUFA9 [mitochondrial matrix]
(Sus scrofa)
ndufa9 [mitochondrial matrix]
(Dictyostelium discoideum)
ndufa9 [mitochondrial matrix]
(Xenopus tropicalis)
nduf-9 [mitochondrial matrix]
(Caenorhabditis elegans)
Ghost homologue of NDUFA9 [mitochondrial matrix]
(Danio rerio)
Ndufa9 [mitochondrial matrix]
(Mus musculus)
Ndufa9 [mitochondrial matrix]
(Rattus norvegicus)
Cross References
ENSEMBL
ENST00000266544
,
ENSP00000266544
OpenTargets
ENSG00000139180
HPA
ENSG00000139180-NDUFA9
PRO
Q16795
Pharos - Targets
Q16795
GlyGen
Q16795
HMDB Protein
HMDBP00177
PDB
5XTH
,
5XTI
,
5XTB
,
5XTD
Interactors (13)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.788
10
UniProt:P19404 NDUFV2
1
NDUFV2 [mitochondrial inner membrane]
(R-HSA-163939)
0.669
5
UniProt:P42858 HTT
1
HTT [nucleoplasm]
(R-HSA-9023590)
0.666
7
UniProt:O75380 NDUFS6
1
NDUFS6 [mitochondrial inner membrane]
(R-HSA-163922)
0.643
6
UniProt:P03915 MT-ND5
1
MT-ND5 [mitochondrial inner membrane]
(R-HSA-60565)
0.527
3
UniProt:Q9UI09 NDUFA12
1
NDUFA12 [mitochondrial inner membrane]
(R-HSA-59864)
0.527
4
UniProt:P56181 NDUFV3
1
NDUFV3 [mitochondrial inner membrane]
(R-HSA-163943)
0.527
4
UniProt:O43920 NDUFS5
1
NDUFS5 [mitochondrial inner membrane]
(R-HSA-60226)
0.527
2
UniProt:O43181 NDUFS4
1
NDUFS4 [mitochondrial inner membrane]
(R-HSA-163946)
0.527
4
UniProt:Q9P0J0 NDUFA13
8
NDUFA13 [mitochondrial inner membrane]
(R-HSA-59936)
NDUFA13(41-49) [mitochondrial inner membrane]
(R-HSA-9839958)
NDUFA13(100-108) [mitochondrial inner membrane]
(R-HSA-9839959)
NDUFA13(109-144) [mitochondrial inner membrane]
(R-HSA-9839968)
NDUFA13(2-19) [mitochondrial inner membrane]
(R-HSA-9839966)
NDUFA13(69-99) [mitochondrial inner membrane]
(R-HSA-9839964)
NDUFA13(20-40) [mitochondrial inner membrane]
(R-HSA-9839963)
NDUFA13(50-68) [mitochondrial inner membrane]
(R-HSA-9839961)
0.527
2
UniProt:P49821 NDUFV1
1
NDUFV1 [mitochondrial inner membrane]
(R-HSA-163926)
0.527
3
UniProt:P78537 BLOC1S1
2
BLOC1S1 [Golgi membrane]
(R-HSA-434324)
BLOC1S1 [lysosomal membrane]
(R-HSA-429821)
0.524
3
UniProt:P10809 HSPD1
6
HSPD1(1-573) [cytosol]
(R-HSA-1267989)
HSPD1(1-573) [mitochondrial intermembrane space]
(R-HSA-1267963)
HSPD1(1-26) [mitochondrial matrix]
(R-HSA-8986171)
HSPD1(1-573) [mitochondrial inner membrane]
(R-HSA-1299442)
HSPD1 [mitochondrial inner membrane]
(R-HSA-1299455)
HSPD1 [mitochondrial matrix]
(R-HSA-1299448)
0.483
3
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