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NDUFA13 [mitochondrial inner membrane]
Stable Identifier
R-HSA-59936
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase B16.6 subunit , Complex I-B16.6, CI-B16.6, Gene associated with retinoic-interferon-induced mortality 19 protein, GRIM-19, Cell death-regulatory protein GRIM-19, CGI-39, CDA016
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
The citric acid (TCA) cycle and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Mitochondrial protein degradation (Homo sapiens)
HTRA2 binds NDUFA13 (GRIM-19) (Homo sapiens)
HTRA2:NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
HTRA2 degrades NDUFA13 (GRIM-19) (Homo sapiens)
HTRA2:NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9P0J0 NDUFA13
Gene Names
NDUFA13, GRIM19, CDA016, CGI-39
Chain
initiator methionine:, chain:2-144
Reference Genes
BioGPS Gene:51079 NDUFA13
COSMIC (genes):NDUFA13 NDUFA13
CTD Gene:51079 NDUFA13
dbSNP Gene:51079 NDUFA13
ENSEMBL:ENSG00000186010 NDUFA13
ENSEMBL_homo_sapiens_GENE:ENSG00000186010.19 NDUFA13
HGNC:17194 NDUFA13
KEGG Gene (Homo sapiens):51079 NDUFA13
Monarch:51079 NDUFA13
NCBI Gene:51079 NDUFA13
OMIM:609435 NDUFA13
UCSC:Q9P0J0 NDUFA13
Reference Transcript
RefSeq:NM_015965.6 NDUFA13
Other Identifiers
11720342_s_at
11757719_x_at
16860047
220864_PM_s_at
220864_s_at
3825826
3825830
3825831
3825833
3825835
3825836
3825837
45339_at
51079
8027205
A_23_P119627
GE82057
GO:0005515
GO:0005524
GO:0005634
GO:0005654
GO:0005737
GO:0005739
GO:0005743
GO:0005746
GO:0005747
GO:0006091
GO:0006351
GO:0006355
GO:0006886
GO:0006915
GO:0007005
GO:0009060
GO:0010952
GO:0012501
GO:0016020
GO:0023052
GO:0030163
GO:0030308
GO:0031966
GO:0032981
GO:0035458
GO:0042776
GO:0043226
GO:0043280
GO:0045039
GO:0045732
GO:0045892
GO:0055086
GO:0061024
GO:0065003
GO:0070469
GO:0071300
GO:0072593
GO:0097190
GO:0097191
GO:1901135
GO:2001243
HMNXSV003044952
PH_hs_0032456
g7705733_3p_a_at
Participates
as an input of
HTRA2 binds NDUFA13 (GRIM-19) (Homo sapiens)
as a component of
HTRA2:NDUFA13 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
Other forms of this molecule
NDUFA13(41-49) [mitochondrial inner membrane]
NDUFA13(100-108) [mitochondrial inner membrane]
NDUFA13(109-144) [mitochondrial inner membrane]
NDUFA13(2-19) [mitochondrial inner membrane]
NDUFA13(69-99) [mitochondrial inner membrane]
NDUFA13(20-40) [mitochondrial inner membrane]
NDUFA13(50-68) [mitochondrial inner membrane]
Inferred To
NDUFA13 [mitochondrial inner membrane]
(Bos taurus)
NDUFA13 [mitochondrial inner membrane]
(Canis familiaris)
NDUFA13 [mitochondrial inner membrane]
(Gallus gallus)
NDUFA13 [mitochondrial inner membrane]
(Sus scrofa)
Ghost homologue of NDUFA13 [mitochondrial inner membrane]
(Danio rerio)
ndufa13 [mitochondrial inner membrane]
(Xenopus tropicalis)
Homologues of NDUFA13 [mitochondrial inner membrane]
(Rattus norvegicus)
Ndufa13 [mitochondrial inner membrane]
(Mus musculus)
Ndufa13 [mitochondrial inner membrane]
(Rattus norvegicus)
Ndufa13-ps1 [mitochondrial inner membrane]
(Rattus norvegicus)
ND-B16.6 [mitochondrial inner membrane]
(Drosophila melanogaster)
ndua-13 [mitochondrial inner membrane]
(Caenorhabditis elegans)
Cross References
RefSeq
NP_057049.5
OpenTargets
ENSG00000186010
HPA
ENSG00000186010-NDUFA13
GeneCards
Q9P0J0
Ensembl
ENSP00000423673
,
ENSG00000186010
,
ENST00000507754
PRO
Q9P0J0
Pharos - Targets
Q9P0J0
Orphanet
22591
HMDB Protein
HMDBP00190
PDB
5XTB
,
5XTC
,
5XTD
,
5XTI
,
5XTH
Interactors (12)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:O43464 HTRA2
1
HTRA2 [mitochondrial intermembrane space]
(R-HSA-56655)
0.674
7
UniProt:P42858 HTT
1
HTT [nucleoplasm]
(R-HSA-9023590)
0.666
4
UniProt:Q9P032 NDUFAF4
1
NDUFAF4 [mitochondrial inner membrane]
(R-HSA-5689124)
0.643
4
UniProt:Q9HC29 NOD2
1
NOD2 [cytosol]
(R-HSA-168411)
0.543
6
UniProt:O75251 NDUFS7
1
NDUFS7 [mitochondrial matrix]
(R-HSA-6788521)
0.527
2
UniProt:Q9UI09 NDUFA12
1
NDUFA12 [mitochondrial inner membrane]
(R-HSA-59864)
0.527
3
UniProt:Q9BQ95 ECSIT
2
ECSIT [cytosol]
(R-HSA-168064)
ECSIT [mitochondrial inner membrane]
(R-HSA-5689047)
0.527
2
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.527
6
UniProt:O43181 NDUFS4
1
NDUFS4 [mitochondrial inner membrane]
(R-HSA-163946)
0.527
2
UniProt:Q9Y375 NDUFAF1
1
NDUFAF1 [mitochondrial inner membrane]
(R-HSA-5689050)
0.527
2
UniProt:O95298 NDUFC2
3
NDUFC2 [plasma membrane]
(R-HSA-6806276)
NDUFC2 [azurophil granule membrane]
(R-HSA-6799211)
NDUFC2 [mitochondrial inner membrane]
(R-HSA-59860)
0.527
2
UniProt:Q9H845 ACAD9
1
ACAD9 [mitochondrial inner membrane]
(R-HSA-5689049)
0.527
2
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