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NDUFV1 [mitochondrial inner membrane]
Stable Identifier
R-HSA-163926
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase 51 kDa subunit
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
NDUF subunits bind to form the FP subcomplex (Homo sapiens)
FP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFV1:4Fe-4S:FMN [mitochondrial inner membrane] (Homo sapiens)
NDUFV1 [mitochondrial inner membrane] (Homo sapiens)
NDUFV1:4Fe-4S:FMN [mitochondrial inner membrane] (Homo sapiens)
NDUFV1 [mitochondrial inner membrane] (Homo sapiens)
NUBPL transfers 4Fe-4S to NDUFV1, V2 (Homo sapiens)
NDUFV1 [mitochondrial inner membrane] (Homo sapiens)
NDUFV1:4Fe-4S:FMN [mitochondrial inner membrane] (Homo sapiens)
NDUFV1 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
FP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFV1:4Fe-4S:FMN [mitochondrial inner membrane] (Homo sapiens)
NDUFV1 [mitochondrial inner membrane] (Homo sapiens)
FP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFV1:4Fe-4S:FMN [mitochondrial inner membrane] (Homo sapiens)
NDUFV1 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
FP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFV1:4Fe-4S:FMN [mitochondrial inner membrane] (Homo sapiens)
NDUFV1 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
FP subcomplex (-NDUFAF2) [mitochondrial inner membrane] (Homo sapiens)
NDUFV1:4Fe-4S:FMN [mitochondrial inner membrane] (Homo sapiens)
NDUFV1 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
FP subcomplex (-NDUFAF2) [mitochondrial inner membrane] (Homo sapiens)
NDUFV1:4Fe-4S:FMN [mitochondrial inner membrane] (Homo sapiens)
NDUFV1 [mitochondrial inner membrane] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Mitochondrial protein degradation (Homo sapiens)
LONP1 binds mitochondrial inner membrane proteins (Homo sapiens)
LONP1:substrate protein (mitochondrial inner membrane) [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
NDUFV1 [mitochondrial inner membrane] (Homo sapiens)
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
NDUFV1 [mitochondrial inner membrane] (Homo sapiens)
LONP1 degrades mitochondrial inner membrane proteins (Homo sapiens)
LONP1:substrate protein (mitochondrial inner membrane) [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
NDUFV1 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:P49821 NDUFV1
Gene Names
NDUFV1, UQOR1
Chain
transit peptide:1-20, chain:21-464
Reference Genes
BioGPS Gene:4723 NDUFV1
COSMIC (genes):NDUFV1 NDUFV1
CTD Gene:4723 NDUFV1
dbSNP Gene:4723 NDUFV1
ENSEMBL:ENSG00000167792 NDUFV1
HGNC:7716 NDUFV1
KEGG:hsa:4723 NDUFV1
Monarch:4723 NDUFV1
NCBI Gene:4723 NDUFV1
OMIM:161015 NDUFV1
UCSC:P49821 NDUFV1
Reference Transcript
RefSeq:NM_001166102.1 NDUFV1
RefSeq:NM_007103.3 NDUFV1
Other Identifiers
11717759_a_at
16727933
16727936
208714_PM_at
208714_at
3337197
3337198
3337199
3337200
3337202
3337203
3337204
3337205
3337206
3337207
3337208
3337209
3337210
3337211
3337212
3337213
3337214
3337215
3337216
3337217
3337218
3337219
3337220
3337221
3337222
3337223
3337224
37329_at
4723
7941946
A_14_P132982
A_14_P139762
A_23_P127353
A_33_P3317406
GE56951
GE61418
GE81726
GO:0003824
GO:0005215
GO:0005515
GO:0005739
GO:0005743
GO:0005829
GO:0006091
GO:0006120
GO:0008137
GO:0009060
GO:0010181
GO:0016491
GO:0042775
GO:0042776
GO:0043226
GO:0045271
GO:0046872
GO:0051287
GO:0051539
GO:0055085
GO:0055086
GO:1901135
GO:1902600
HMNXSV003015140
HMNXSV003021642
ILMN_1786718
ILMN_1870931
PH_hs_0000797
TC11000695.hg
TC11000696.hg
g5138911_3p_at
p2806
Participates
as a member of
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
as an input of
NUBPL transfers 4Fe-4S to NDUFV1, V2 (Homo sapiens)
as a component of
NDUFV1:4Fe-4S:FMN [mitochondrial inner membrane] (Homo sapiens)
Inferred To
nuo-1 [mitochondrial inner membrane]
(Caenorhabditis elegans)
ndufv1 [mitochondrial inner membrane]
(Danio rerio)
ndufv1 [mitochondrial inner membrane]
(Xenopus tropicalis)
Homologues of NDUFV1 [mitochondrial inner membrane]
(Xenopus tropicalis)
ND-51 [mitochondrial inner membrane]
(Drosophila melanogaster)
Ghost homologue of NDUFV1 [mitochondrial inner membrane]
(Gallus gallus)
NDUFV1 [mitochondrial inner membrane]
(Bos taurus)
NDUFV1 [mitochondrial inner membrane]
(Canis familiaris)
NDUFV1 [mitochondrial inner membrane]
(Dictyostelium discoideum)
NDUFV1 [mitochondrial inner membrane]
(Mus musculus)
NDUFV1 [mitochondrial inner membrane]
(Schizosaccharomyces pombe)
NDUFV1 [mitochondrial inner membrane]
(Sus scrofa)
Ndufv1 [mitochondrial inner membrane]
(Rattus norvegicus)
Cross References
ENSEMBL
ENST00000647561
,
ENSP00000497587
,
ENST00000529927
,
ENST00000322776
,
ENSP00000322450
,
ENSP00000436766
OpenTargets
ENSG00000167792
HPA
ENSG00000167792-NDUFV1
PRO
P49821
Pharos - Targets
P49821
GlyGen
P49821
Orphanet
NDUFV1
PDB
5XTH
,
5XTI
,
5XTD
,
5XTB
HMDB Protein
HMDBP00186
Interactors (33)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P56181 NDUFV3
1
NDUFV3 [mitochondrial inner membrane]
(R-HSA-163943)
0.669
5
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.643
7
UniProt:O43678 NDUFA2
1
NDUFA2 [mitochondrial inner membrane]
(R-HSA-60178)
0.564
3
UniProt:Q9Y297 BTRC
2
BTRC [cytosol]
(R-HSA-174237)
BTRC [nucleoplasm]
(R-HSA-3361753)
0.556
3
UniProt:A8MQ03 CRTP1
0.556
3
UniProt:P17252 PRKCA
8
PRKCA [cytosol]
(R-HSA-58196)
PRKCA [plasma membrane]
(R-HSA-156469)
pT497,T638,S657-PRKCA [plasma membrane]
(R-HSA-4332340)
p-T497,T638,S657-PRKCA [nucleoplasm]
(R-HSA-5223292)
p-T497-PRKCA [cytosol]
(R-HSA-5218731)
p-T497,T638,S657-PRKCA [cytosol]
(R-HSA-4332337)
PRKCA [photoreceptor disc membrane]
(R-HSA-2648987)
PRKCA [nucleoplasm]
(R-HSA-450530)
0.556
3
UniProt:P25788-2 PSMA3
0.556
3
UniProt:Q8TCJ0-3 FBXO25
0.556
3
UniProt:Q8IZU1 FAM9A
0.556
3
UniProt:Q15047-2 SETDB1
0.556
3
UniProt:Q8WUA7-2 Q8WUA72
0.556
3
UniProt:Q92993 KAT5
1
KAT5 [nucleoplasm]
(R-HSA-3321979)
0.556
3
UniProt:P61981 YWHAG
1
YWHAG [cytosol]
(R-HSA-380312)
0.556
3
UniProt:P20618 PSMB1
7
PSMB1 [cytosol]
(R-HSA-68738)
PSMB1 [nucleoplasm]
(R-HSA-174347)
PSMB1 [secretory granule lumen]
(R-HSA-6803287)
PSMB1 [extracellular region]
(R-HSA-6806477)
PSMB1 [ficolin-1-rich granule lumen]
(R-HSA-6803340)
pro-PSMB1 [cytosol]
(R-HSA-9908139)
PSMB1(1-28) [cytosol]
(R-HSA-9908143)
0.556
3
UniProt:P41218 MNDA
3
MNDA [ficolin-1-rich granule lumen]
(R-HSA-6800897)
MNDA [extracellular region]
(R-HSA-6806244)
MNDA [azurophil granule lumen]
(R-HSA-6799237)
0.556
3
UniProt:P61201 COPS2
2
COPS2 [cytosol]
(R-HSA-416971)
COPS2 [nucleoplasm]
(R-HSA-5697012)
0.556
3
UniProt:Q16401 PSMD5
1
PSMD5 [cytosol]
(R-HSA-68802)
0.556
3
UniProt:Q8TAP4-4 LMO3
0.556
3
UniProt:Q96B65 Q96B65
0.556
3
UniProt:Q2TAY7 SMU1
1
SMU1 [nucleoplasm]
(R-HSA-9770259)
0.556
3
UniProt:P45880 VDAC2
6
p-S65-Ub:VDAC2 [mitochondrial outer membrane]
(R-HSA-9834982)
K63polyUb-VDAC2 [mitochondrial outer membrane]
(R-HSA-9843314)
K48polyUb-VDAC2 [mitochondrial outer membrane]
(R-HSA-9843321)
Ub-VDAC2 [mitochondrial outer membrane]
(R-HSA-9835025)
VDAC2 [mitochondrial outer membrane]
(R-HSA-5696880)
PolyUb-VDAC2 [mitochondrial outer membrane]
(R-HSA-6783185)
0.556
3
UniProt:Q9NP61 ARFGAP3
1
ARFGAP3 [cytosol]
(R-HSA-6807740)
0.556
3
UniProt:Q7Z6E9-3 RBBP6
0.556
3
UniProt:Q96CV9-2 OPTN
0.556
3
UniProt:Q9NTX7-2 RNF146
0.556
3
UniProt:Q9H871 RMND5A
1
RMND5A [cytosol]
(R-HSA-9861580)
0.556
3
UniProt:Q6P3S6 FBX42
0.556
3
UniProt:Q99932-2 SPAG8
0.556
3
UniProt:Q16795 NDUFA9
1
NDUFA9 [mitochondrial matrix]
(R-HSA-163942)
0.527
3
UniProt:O43920 NDUFS5
1
NDUFS5 [mitochondrial inner membrane]
(R-HSA-60226)
0.527
2
UniProt:P19404 NDUFV2
1
NDUFV2 [mitochondrial inner membrane]
(R-HSA-163939)
0.527
3
UniProt:O75380 NDUFS6
1
NDUFS6 [mitochondrial inner membrane]
(R-HSA-163922)
0.527
4
UniProt:Q9P0J0 NDUFA13
8
NDUFA13 [mitochondrial inner membrane]
(R-HSA-59936)
NDUFA13(41-49) [mitochondrial inner membrane]
(R-HSA-9839958)
NDUFA13(100-108) [mitochondrial inner membrane]
(R-HSA-9839959)
NDUFA13(109-144) [mitochondrial inner membrane]
(R-HSA-9839968)
NDUFA13(2-19) [mitochondrial inner membrane]
(R-HSA-9839966)
NDUFA13(69-99) [mitochondrial inner membrane]
(R-HSA-9839964)
NDUFA13(20-40) [mitochondrial inner membrane]
(R-HSA-9839963)
NDUFA13(50-68) [mitochondrial inner membrane]
(R-HSA-9839961)
0.527
2
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